Any total absence of embryo-fetal development of lymphatic structures is practically incompatible with extrauterine life.The majority of congenital clinical manifestations, due to a development deficit of lymphatic structures, are most commonly correlated with anatomic-pathologic pictures of lymphatic structures-lymph node hypoplasia, or, in very rare cases, partial aplasia of major lymphatic structures, such as, for example, the thoracic duct.